Phase 3 Wilson Disease Trial, Terminated NCT03403205 Sponsor: Alexion Pharmaceuticals, Inc. Condition: Wilson Disease
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Trial results

AI generated results summary. Written by an AI model from the official source data and checked on a sample basis. It can contain mistakes, so confirm anything important against the original source. How we use AI

According to the results reported on ClinicalTrials.gov, this trial enrolled people with Wilson disease — a condition where the body accumulates too much copper. Participants were split into two cohorts based on whether they had mainly neurological (nerve and brain-related) or hepatic (liver-related) symptoms. Within each cohort, people were randomly assigned to receive either the investigational medicine ALXN1840 or a standard-of-care (SoC) therapy — meaning the treatments already commonly used for Wilson disease. In total, 105 people started in Cohort 1 on ALXN1840, 56 in Cohort 1 on SoC, 37 in Cohort 2 on ALXN1840, and 16 in Cohort 2 on SoC, across a 48-week main study period followed by a longer extension phase of up to 60 months. The trial's main focus was measuring levels of a particular form of copper in the blood — called non-ceruloplasmin-bound copper (essentially the "free" copper not attached to a carrier protein) — over the 48 weeks. The reported data shows that for the primary measure — the average daily level of free copper in the blood over 48 weeks — the ALXN1840 groups recorded higher values than the SoC groups. Specifically, the reported figures were 2.50 units for Cohort 1 on ALXN1840 versus 0.87 units for Cohort 1 on SoC, and 4.76 units for Cohort 2 on ALXN1840 versus 0.96 units for Cohort 2 on SoC (measured in micromoles per litre, averaged across hours). For the secondary measures, changes in neurological symptom scores (rated on a scale where lower numbers mean improvement) were also reported at 48 weeks. In Cohort 1, the ALXN1840 group's neurological examination score changed by −2.24 points and the SoC group by −1.59 points. In Cohort 2, the ALXN1840 group changed by −2.06 points while the SoC group's score increased by +1.55 points. Self-reported daily functioning scores showed small changes across all groups. The reported data also shows that 89 out of 104 participants who received ALXN1840 in Cohort 1, 41 out of 56 in the Cohort 1 SoC group, 30 out of 33 in Cohort 2 on ALXN1840, and 12 out of 14 in the Cohort 2 SoC group experienced at least one adverse event (an unwanted medical occurrence during the study period) — though the data does not specify the nature or severity of those events in this summary. These are the results as reported to ClinicalTrials.gov. They are not medical advice — always discuss what they mean for you with your doctor.

These are the results as reported to ClinicalTrials.gov, not medical advice. Verify independently with the trial site and discuss what they mean for you with your doctor.

Phase 3 Wilson Disease Trial, Terminated

NCT03403205
Terminated Phase 3 🇦🇺 Australian site

Who may be able to join

AI generated eligibility summary. Written by an AI model from the official source data and checked on a sample basis. It can contain mistakes, so confirm anything important against the original source. How we use AI

Who might be able to join this trial:

  • You have been diagnosed with Wilson's disease, confirmed by a scoring system called the Leipzig Score (a score of 4 or higher)
  • If you are a woman of childbearing age and are sexually active with a male partner, you are willing to use highly effective birth control starting at least 6 weeks before the trial begins and for 28 days after your last dose of study medication
  • If you are a man and are sexually active with a female partner, you are willing to use highly effective birth control from the first day of the trial and for 90 days after your last dose of study medication

Who may not be able to join:

  • You have severe liver scarring (cirrhosis) where the liver is no longer able to function properly
  • Your liver disease severity score (called a MELD score) is higher than 13 (confirm with trial site)
  • Your liver disease score on another measure (called the Modified Nazer score) is higher than 7 (confirm with trial site)
  • You have had a significant bleeding episode in your digestive system (such as stomach or intestines) in the past 3 months
  • Your liver enzyme levels (called ALT) are too high — the exact limit depends on how long you have already been treated for Wilson's disease (confirm with trial site)
  • You have severe neurological symptoms requiring tube feeding or intensive hospital care
  • Your red blood cell count is too low (a hemoglobin level below 9 grams per deciliter)
  • You have had seizures in the 6 months before joining the trial
  • You are pregnant, planning to become pregnant, or are currently breastfeeding
  • You have an active hepatitis B or hepatitis C infection, or you are HIV positive
  • You have previously been treated with a medication called tetrathiomolybdate
  • You have very severe kidney disease requiring dialysis, or your kidneys are not filtering blood well enough (confirm with trial site)

Important: Always verify eligibility with the trial site directly before applying.

Based on publicly available eligibility criteria from ClinicalTrials.gov. Verify directly with the trial site before acting. This is not medical advice.

This is a simplified plain English summary of the eligibility criteria. Full criteria are set by the trial investigators and may include additional requirements not shown here. Never self-exclude from a trial based on this summary. Contact the trial site directly to confirm your eligibility.
Last synced 28 July 2026
Phase 3: approximately ~65% of drugs entering this phase reach regulatory approval, based on published industry-wide historical data. This is not specific to this trial.
Phase success rates shown are historical industry-wide averages based on published data. They are not a prediction for this specific trial or your individual situation.

Contact this trial

Principal Investigator: Eugene S. Swenson, M.D., Ph.D., Alexion Pharmaceuticals, Inc.

Australian sites

Research Site, Adelaide,
Research Site, Concord,
Research Site, Parkville,
Research Site, Parkville,

Contact details sourced from ClinicalTrials.gov. Verify directly with the trial site before attending.

GP referral letter

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Trial details

Status
Terminated
Phase
Phase 3
Sponsor
Alexion Pharmaceuticals, Inc.
Registry
ClinicalTrials.gov
Start date
22 February 2018
Est. completion
30 June 2023

Where this trial is recruiting

🇦🇺 Australia 🇦🇹 Austria 🇨🇦 Canada 🇨🇿 Czechia 🇩🇰 Denmark 🇫🇷 France 🇩🇪 Germany Hong Kong 🇭🇺 Hungary 🇮🇱 Israel 🇯🇵 Japan 🇳🇿 New Zealand 🇵🇱 Poland 🇷🇺 Russia 🇷🇸 Serbia 🇸🇬 Singapore 🇰🇷 South Korea 🇪🇸 Spain 🇹🇼 Taiwan Turkey (Türkiye) 🇬🇧 United Kingdom 🇺🇸 United States

4 site(s) in Australia. Confirm current status and contact details directly with the trial site.

Primary endpoints

Daily Mean Area Under The Effect-time Curve (AUEC) of Directly Measured Non-ceruloplasmin-bound Copper (dNCC) From 0 to 48 Weeks (dNCC AUEC0-48W)

Can't join this trial?

Expanded access pathways

If this trial is not available to you, other access pathways may exist. In Australia, the TGA Special Access Scheme allows access to unapproved therapeutic goods for individual patients.

TGA Special Access Scheme information

Find other recruiting trials on ClinicalTrials.gov

Data last synced from ClinicalTrials.gov: 28 July 2026. Trial status can change. Always verify current status directly with the trial site before making any decision.

Trial recruitment status can change without notice between our nightly data updates. Always contact the trial site directly to confirm current recruitment status before making any decisions or travel arrangements.

View original record on ClinicalTrials.gov