Phase 2 Muscular Dystrophy Trial, Completed NCT00592553 Sponsor: PTC Therapeutics Condition: Muscular Dystrophy
Back to Muscular Dystrophy

Trial results

AI generated results summary. Written by an AI model from the official source data and checked on a sample basis. It can contain mistakes, so confirm anything important against the original source. How we use AI

According to the results reported on ClinicalTrials.gov, this trial enrolled 174 boys with Duchenne muscular dystrophy — a condition caused by a specific type of genetic change called a nonsense mutation. Sixty participants received a high dose of a medicine called ataluren, 57 received a low dose, and 57 received a placebo (a dummy treatment with no active ingredient). The trial ran for 48 weeks. The main thing being measured was how far participants could walk in six minutes (known as the "6-minute walk distance" or 6MWD) — a standard way of tracking movement ability in these trials. The reported data shows that over the 48 weeks, the distance walked in six minutes changed in all three groups. On average, the high-dose ataluren group's walking distance decreased by about 42 metres, the placebo group's decreased by about 43 metres, and the low-dose ataluren group's decreased by about 13 metres. For the secondary measures — which included how long it took to stand up from lying down, walk or run 10 metres, climb four stairs, and descend four stairs — the reported data shows that times increased (meaning tasks took longer) across all three groups by the end of the study. Muscle strength, measured in pounds of force across several muscle groups in the arms and legs, also showed small changes across all groups; the specific numbers varied by muscle group and are listed in the full data set on ClinicalTrials.gov. Where baseline (starting point) figures appear duplicated in the raw data, this reflects how the data was structured in the submission, and readers should refer to the full record for complete context. These are the results as reported to ClinicalTrials.gov. They are not medical advice — always discuss what they mean for you with your doctor.

These are the results as reported to ClinicalTrials.gov, not medical advice. Verify independently with the trial site and discuss what they mean for you with your doctor.

Phase 2 Muscular Dystrophy Trial, Completed

NCT00592553
Completed Phase 2 🇦🇺 Australian site

Who may be able to join

AI generated eligibility summary. Written by an AI model from the official source data and checked on a sample basis. It can contain mistakes, so confirm anything important against the original source. How we use AI

Who might be able to join this trial:

  • You are able to read and sign a consent form (or a parent/guardian can sign on your behalf if you are under 18)
  • You are male
  • You are 5 years of age or older
  • You have shown signs of Duchenne or Becker muscular dystrophy (such as muscle weakness, an unusual walking style, or difficulty getting up from the floor) before age 9, along with high levels of a muscle enzyme in your blood and ongoing difficulty walking
  • A genetic test has confirmed that your dystrophy is caused by a specific type of gene change called a "nonsense mutation" in the dystrophin gene, tested by an approved laboratory
  • A blood sample has been taken to confirm the presence of this specific gene change
  • You are able to walk at least 75 meters (about 246 feet) on your own without any personal help or walking aids during a 6-minute walk test
  • Your blood test results for liver, kidney, adrenal gland, and electrolyte levels are within normal ranges
  • If you are sexually active, you are willing to abstain from sex or use contraception during the treatment period and for 6 weeks after
  • You are willing and able to attend all scheduled visits and follow all study procedures and rules

Who may not be able to join:

  • You have been treated with a type of antibiotic called aminoglycosides (given throughout the body, not just topically) in the past 3 months
  • You started taking steroid medication (such as prednisone) in the past 6 months, or your steroid dose or schedule changed in the past 3 months
  • Any medication you take for heart failure has been started, changed, or stopped in the past 3 months
  • You have taken the blood-thinning medication warfarin in the past month
  • You have previously received the study drug ataluren
  • You have a known allergy to any ingredient in the study drug (confirm with trial site)
  • You have taken part in another clinical trial involving an experimental drug in the past 2 months
  • You have had a major surgery in the past 30 days
  • You are currently taking immune-suppressing medication (other than steroids)
  • You are currently taking part in another treatment clinical trial
  • You are expected to need major surgery (for example, surgery for a curved spine) during the 12-month study period
  • You need a ventilator (breathing machine) to help you breathe during the day
  • You have significant heart failure symptoms or your heart scan shows serious heart muscle problems
  • You have another medical, mental health, or personal condition that, in the doctor's opinion, could affect your safety, your ability to complete the study, or the accuracy of the results

Important: Always verify eligibility with the trial site directly before applying.

Based on publicly available eligibility criteria from ClinicalTrials.gov. Verify directly with the trial site before acting. This is not medical advice.

This is a simplified plain English summary of the eligibility criteria. Full criteria are set by the trial investigators and may include additional requirements not shown here. Never self-exclude from a trial based on this summary. Contact the trial site directly to confirm your eligibility.
Last synced 26 July 2026
Phase 2: approximately ~30% of drugs entering this phase reach regulatory approval, based on published industry-wide historical data. This is not specific to this trial.
Phase success rates shown are historical industry-wide averages based on published data. They are not a prediction for this specific trial or your individual situation.

Contact this trial

Principal Investigator: Leone Atkinson, MD, PhD, PTC Therapeutics

Australian sites

Royal Children's Hospital, Parkville, Victoria
Institute For Neuromuscular Research, The Children's Hospital at Westmead, Westmead,

Contact details sourced from ClinicalTrials.gov. Verify directly with the trial site before attending.

GP referral letter

Print a one-page summary to share with your doctor.

Trial details

Status
Completed
Phase
Phase 2
Sponsor
PTC Therapeutics
Registry
ClinicalTrials.gov
Start date
29 February 2008
Est. completion
31 December 2009

Where this trial is recruiting

🇦🇺 Australia 🇧🇪 Belgium 🇨🇦 Canada 🇫🇷 France 🇩🇪 Germany 🇮🇱 Israel 🇮🇹 Italy 🇪🇸 Spain 🇸🇪 Sweden 🇬🇧 United Kingdom 🇺🇸 United States

2 site(s) in Australia. Confirm current status and contact details directly with the trial site.

Primary endpoints

Change From Baseline in 6MWD at Week 48

Can't join this trial?

Expanded access pathways

If this trial is not available to you, other access pathways may exist. In Australia, the TGA Special Access Scheme allows access to unapproved therapeutic goods for individual patients.

TGA Special Access Scheme information

Find other recruiting trials on ClinicalTrials.gov

Data last synced from ClinicalTrials.gov: 26 July 2026. Trial status can change. Always verify current status directly with the trial site before making any decision.

Trial recruitment status can change without notice between our nightly data updates. Always contact the trial site directly to confirm current recruitment status before making any decisions or travel arrangements.

View original record on ClinicalTrials.gov